Metastatic Alveolar Soft Part Sarcoma.

Park, Se Hyuck; Lee, Kyu Ho; Rhim, Hyo Keun; Lee, Kil Woo; Shin, Hyung Sik; Kang, Gu; Shin, Bo Chul

Original Article

Journal of Korean Neurosurgical Society 1991;20(1-3): 116-123.

Se Hyuck Park, Kyu Ho Lee, Hyo Keun Rhim, Kil Woo Lee, Hyung Sik Shin, Gu Kang, Bo Chul Shin

¹Department of Neurosurgery, Kangdong Sacred Heart Hospital College of Medicine, Hallym University, Seoul, Korea.
²Department of Radiology, Kangdong Sacred Heart Hospital College of Medicine, Hallym University, Seoul, Korea.
³Department of Pathology, Kangdong Sacred Heart Hospital College of Medicine, Hallym University, Seoul, Korea.

ABSTRACT

A case of metastatic alveolar soft part sarcoma is presented with clincal, pathological and radiological features. Alveolar soft part sarcoma is a rare soft-tissue neoplasm that is malignant and invariably fatal. It was first described and named by Christopherson, et al. in 1952. Since 1952 numerous examples of this tumor have been reported and have been studied with the electron microscope, but there is still considerable uncertainty as to the exact histogenesis of the tumor. Most cases occur in young females involving the lower extrimities especially in the right side. The most initial presenting symptom is a slowgrowing painless mass and the principal metastatic sites are the lungs, followed by the brain and skeleton. Cerebral metastasis, in fact, may be the first manifestation of the disease. Treatment is radical surgical excision but radiotherapy and chemotherapy are less effective. We present the reported case of metastatic alveolar soft pat sarcoma with electron microscopic findings.

Key Words: Alveolar soft part sarcoma; Painless mass; Metastasis; Radical excision