Bilateral Large Thoracic Neuofibromas in Type I Neurofibromatosis.

Park, Sukh Que; Chang, Jae Chil; Doh, Jae Won; Kim, Bum Tae; Shin, Won Han; Choi, Soon Kwan; Byun, Bark Jang; Lee, Man Bok; Koh, Eun Suk

Case Report

Journal of Korean Neurosurgical Society 1999;28(1): 92-96.

Sukh Que Park, Jae Chil Chang, Jae Won Doh, Bum Tae Kim, Won Han Shin, Soon Kwan Choi, Bark Jang Byun, Man Bok Lee, Eun Suk Koh

¹Department of Neurosurgery, College of Medicine, Soonchunhyang University, Seoul, Korea.
²Department of Chest Surgery, College of Medicine, Soonchunhyang University, Seoul, Korea.
³Department of Anatomic Pathology, College of Medicine, Soonchunhyang University, Seoul, Korea.

ABSTRACT

Type 1 Neurofibromatosis(von Recklinghausen's disease) characterized by cafe-au-lait spot and multiple skin nodules, may involve any part of the body. The incidence of multiple spinal neurofibromas is about 15% of all spinal neurofibromas and the majority of them are located in cauda equina. However, thoracic spine is uncommon site of multiple spinal neurofibrmas in type 1 neurofibromatosis. The authors describe a case of bilateral large neurofibromas of the thoracic spine associated with type 1 neurofibromatosis in a 27-year-old man.